Journal of Cystic Fibrosis

Titel Veröffentlichungsdatum Sprache Zitate
ECFS best practice guidelines: the 2018 revision2018/03/01English482
Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice2008/05/01English386
European Cystic Fibrosis Society Standards of Care: Best Practice guidelines2014/05/01English361
Treatment of lung infection in patients with cystic fibrosis: Current and future strategies2012/12/01English351
High treatment burden in adults with cystic fibrosis: Challenges to disease self-management2009/03/01English332
Inflammation in cystic fibrosis lung disease: Pathogenesis and therapy2015/07/01English307
Ivacaftor potentiation of multiple CFTR channels with gating mutations2012/05/01English303
Standards of care for patients with cystic fibrosis: a European consensus2005/03/01English292
Chronic Mycobacterium abscessus infection and lung function decline in cystic fibrosis2010/03/01English281
Efficacy and safety of ivacaftor in patients with cystic fibrosis and a non-G551D gating mutation2014/12/01English279
The prevalence of cystic fibrosis in the European Union2008/09/01English263
Effect of ivacaftor on CFTR forms with missense mutations associated with defects in protein processing or function2014/01/01English247
Induction of cathelicidin in normal and CF bronchial epithelial cells by 1,25-dihydroxyvitamin D32007/11/01English241
Safety, efficacy and convenience of tobramycin inhalation powder in cystic fibrosis patients: The EAGER trial2011/01/01English235
Pseudomonas aeruginosa lasR mutants are associated with cystic fibrosis lung disease progression2009/01/01English212
Early intervention and prevention of lung disease in cystic fibrosis: a European consensus2004/06/01English209
A multi-method assessment of treatment adherence for children with cystic fibrosis2006/08/01English181
Prevalence and antimicrobial susceptibility of microorganisms isolated from sputa of patients with cystic fibrosis2008/03/01English176
Inhaled medication and inhalation devices for lung disease in patients with cystic fibrosis: A European consensus2009/09/01English175
Disease progression in patients with cystic fibrosis treated with ivacaftor: Data from national US and UK registries2020/01/01English174
CFTR modulator theratyping: Current status, gaps and future directions2019/01/01English174
Innate immunity in cystic fibrosis lung disease2012/09/01English173
Eradication of early Pseudomonas aeruginosa infection2005/08/01English163
The role of respiratory viruses in cystic fibrosis2008/07/01English163
European best practice guidelines for cystic fibrosis neonatal screening2009/05/01English157
Early aggressive eradication therapy for intermittent Pseudomonas aeruginosa airway colonization in cystic fibrosis patients: 15 years experience2008/11/01English156
A survey of newborn screening for cystic fibrosis in Europe2007/01/01English152
Ultrastructural characterization of cystic fibrosis sputum using atomic force and scanning electron microscopy2012/03/01English148
Lung clearance index: Evidence for use in clinical trials in cystic fibrosis2014/03/01English148
Review: Staphylococcus aureus and MRSA in cystic fibrosis2011/09/01English147