Journal of Cystic Fibrosis

Title Publication Date Language Citations
Longitudinal association between medication adherence and lung health in people with cystic fibrosis2011/07/01English147
Emerging bacterial pathogens and changing concepts of bacterial pathogenesis in cystic fibrosis2015/05/01English142
Up-to-date and projected estimates of survival for people with cystic fibrosis using baseline characteristics: A longitudinal study using UK patient registry data2018/03/01English140
Airway glucose concentrations and effect on growth of respiratory pathogens in cystic fibrosis2007/04/01English138
European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre2014/05/01English136
The relative frequency of CFTR mutation classes in European patients with cystic fibrosis2014/07/01English130
Cirrhosis and other liver disease in cystic fibrosis2013/03/01English129
Update on cystic fibrosis-related diabetes2013/07/01English128
Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): A new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening2015/11/01English128
Established cell lines used in cystic fibrosis research2004/08/01English126
Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines2019/05/01English126
Pancreatic insufficiency in Cystic Fibrosis2017/11/01English119
Inflammation in Achromobacter xylosoxidans infected cystic fibrosis patients2010/01/01English118
Achromobacter xylosoxidans in cystic fibrosis: Prevalence and clinical relevance2007/01/01English117
Targeting ion channels in cystic fibrosis2015/09/01English114
Metagenomics and metatranscriptomics: Windows on CF-associated viral and microbial communities2013/03/01English113
Worldwide rates of diagnosis and effective treatment for cystic fibrosis2022/05/01English111
Sweat chloride as a biomarker of CFTR activity: Proof of concept and ivacaftor clinical trial data2014/03/01English110
Treatment complexity in cystic fibrosis: Trends over time and associations with site-specific outcomes2013/09/01English109
Spread of colistin resistant non-mucoid Pseudomonas aeruginosa among chronically infected Danish cystic fibrosis patients2008/09/01English107
Sputum and serum calprotectin are useful biomarkers during CF exacerbation2010/05/01English106
Inhaled aztreonam lysine vs. inhaled tobramycin in cystic fibrosis: A comparative efficacy trial2013/03/01English105
Guidelines for the management of pregnancy in women with cystic fibrosis2008/01/01English103
A randomized double blind, placebo controlled phase 2 trial of BIIL 284 BS (an LTB4 receptor antagonist) for the treatment of lung disease in children and adults with cystic fibrosis2014/03/01English103
β-defensins and LL-37 in bronchoalveolar lavage fluid of patients with cystic fibrosis2004/03/01English103
Prevalence and risk factors for recovery of filamentous fungi in individuals with cystic fibrosis2010/03/01English101
Does bacterial density in cystic fibrosis sputum increase prior to pulmonary exacerbation?2011/09/01English100
Identification and distribution of Achromobacter species in cystic fibrosis2013/05/01English100
A multinational report to characterise SARS-CoV-2 infection in people with cystic fibrosis2020/05/01English99
Increasing nontuberculous mycobacteria infection in cystic fibrosis2015/01/01English99